产品货号：
Z26588
中文名称：
SGSH抗体
英文名称：
Anti-SGSH Antibody
产品规格：
50μl|100μl|150μl
发货周期：
1～3天
产品价格：
询价
| 抗体名称 | Anti-SGSH Antibody |
| 指标别名 | HSS;MPS3A;SFMD;SGSH;Sulfoglucosamine sulfamidase;Sulphamidase |
| 克隆性 | Polyclonal |
| 检验物种 | human |
| 应用范围 | WB,ELISA |
| 基因名称 | SGSH |
| 抗体来源 | Rabbit |
| 抗体类型 | IgG |
| 免疫原 | E.coli-derived human HSS/SGSH recombinant protein (Position:R206-L502). |
| 实际分子量 | 70KD |
| 成分 | 500μg/mL antibody with PBS,0.02% NaN3,1mg BSA and 50% glycerol. |
| 纯化方式 | Immunogen affinity purified. |
| 浓度 | 500μg/mL |
| 产品形态 | 溶液 |
| 保存条件 | 12 months from date of receipt，-20℃ as supplied.6 months 2 to 8℃ after reconstitution.Avoid repeated freezing and thawing. |
| 背景资料 | N-sulphoglucosamine sulphohydrolase is an enzyme that in humans is encoded by the SGSH gene.This gene encodes the enzyme sulfamidase;one of several enzymes involved in the lysosomal degradation of heparan sulfate.Mutations in this gene are associated with the lysosomal storage disease mucopolysaccaridosis IIIA,also known as Sanfilippo syndrome A,which results from impaired degradation of heparan sulfate.Transcripts of varying sizes have been reported but their biological validity has not been determined. |
| Uniprot ID | P51688 |
| 推荐配套试剂 | Biorab recommends Enhanced Chemiluminescent Kit with anti-Rabbit IgG (ZN1926) for Western blot. |
| 基因名全称 | N-sulfoglucosamine sulfohydrolase |
| 蛋白名全称 | N-sulphoglucosamine sulphohydrolase |
| 推荐稀释比 | Western blot(WB) 1:500～2000 ELISA 1:100～1000 |
相关搜索：SGSH抗体，SGSH多抗，Anti-SGSH Antibody